Case Report: persistent diaphragmatic and cardiac involvement despite creatine kinase normalization in anti-mitochondrial M2 antibody-positive inflammatory myopathy with primary biliary cholangitis

Anti-mitochondrial M2 antibodies (AMA-M2) are a serologic hallmark of primary biliary cholangitis (PBC), but in inflammatory myopathy they have also been associated with chronic muscle disease, cardiac involvement, and respiratory muscle weakness. We r…

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