Two Cases of CLIPPERS-like Syndrome Sharing a Hypomorphic UNC13D Variant
J Clin Immunol. 2026 Mar 4;46(1):23. doi: 10.1007/s10875-026-01988-1. NO ABSTRACT PMID:41781714 | DOI:10.1007/s10875-026-01988-1
Journal of Clinical Immunology
Unraveling BCR Repertoire Diversity and its Impact on Glucocorticoid Therapy in Pediatric Idiopathic Nephrotic Syndrome
J Clin Immunol. 2026 Mar 2. doi: 10.1007/s10875-026-01994-3. Online ahead of print. ABSTRACT AIM: Idiopathic nephrotic syndrome (INS) is the most common glomerular disease in children, but its underlying mechanisms remain unclear. Although glucocorticoids (GC) are the first-line treatment, approximately 10% of INS cases are steroid-resistant (SRNS), and 50% may progress to refractory nephrotic syndrome … Read more
Porto-sinusoidal Vascular Disease is Associated with Gastrointestinal Disorders in Common Variable Immunodefiency
J Clin Immunol. 2026 Feb 28. doi: 10.1007/s10875-026-01985-4. Online ahead of print. NO ABSTRACT PMID:41762359 | DOI:10.1007/s10875-026-01985-4
Fatal Systemic Granulomatous Disease Associated with Vaccine-Derived Rubella Virus in AIOLOS-Associated Immunodeficiency
J Clin Immunol. 2026 Feb 26. doi: 10.1007/s10875-026-01990-7. Online ahead of print. NO ABSTRACT PMID:41746515 | DOI:10.1007/s10875-026-01990-7
Primary Immunodeficiency Diseases with BCG-Induced Diseases: A 15-Year Longitudinal Cohort Study
J Clin Immunol. 2026 Feb 26. doi: 10.1007/s10875-026-01996-1. Online ahead of print. NO ABSTRACT PMID:41748971 | DOI:10.1007/s10875-026-01996-1
A Cohort Study of 38 Classic Wiskott-Aldrich Syndrome Cases with Six Novel Mutations
J Clin Immunol. 2026 Feb 20. doi: 10.1007/s10875-026-01986-3. Online ahead of print. NO ABSTRACT PMID:41718912 | DOI:10.1007/s10875-026-01986-3
TFRC Germline Variants and Inborn Error of Immunity: Mechanistic Insights into Iron-Immune Crosstalk
J Clin Immunol. 2026 Feb 20. doi: 10.1007/s10875-026-01999-y. Online ahead of print. NO ABSTRACT PMID:41714512 | DOI:10.1007/s10875-026-01999-y
Good’s Syndrome Mirrors a Combined Immunodeficiency with Anti-Cytokine Antibodies in the Total Absence of B Cells
J Clin Immunol. 2026 Feb 17. doi: 10.1007/s10875-026-01992-5. Online ahead of print. NO ABSTRACT PMID:41701387 | DOI:10.1007/s10875-026-01992-5
Spectrum of Primary Immune Regulatory Disorders in Children in a Highly Consanguineous Population: Report from a National Registry
J Clin Immunol. 2026 Feb 14. doi: 10.1007/s10875-026-01993-4. Online ahead of print. NO ABSTRACT PMID:41688586 | DOI:10.1007/s10875-026-01993-4
WAS Protein Deficiency Disrupts Memory B Cell Formation During Acute LCMV Infection
J Clin Immunol. 2026 Feb 11. doi: 10.1007/s10875-026-01984-5. Online ahead of print. ABSTRACT Wiskott-Aldrich syndrome (WAS) is a rare x-linked monogenic immunodeficiency disease, caused by the mutation of WAS gene encoding WAS protein (WASp). Previous findings in WAS patients show B cell perturbations in the periphery, characterized by diminished B-cell numbers and phenotype abnormalities, including … Read more