NUFIP1 gain of function promotes fibrotic remodeling and reveals a ZNHIT3-linked metabolic vulnerability in idiopathic pulmonary fibrosis models
BackgroundFibroblast activation and extracellular matrix deposition are central features of IPF, but the molecular programs that sustain pathogenic fibroblast states remain incompletely defined. NUFIP1 has been implicated in ribonucleoprotein biology a…